Fibrosis Care

Interstitial Lung Disease (ILD) & Pulmonary Fibrosis

Expert multidisciplinary clinical diagnosis and individualized disease-modifying therapy for Interstitial Lung Disease (ILD), Idiopathic Pulmonary Fibrosis (IPF), Hypersensitivity Pneumonitis, and connective tissue autoimmune lung disease at KIMS Super Speciality Hospital, Electronic City, Bangalore.

+91 70222 23966 OPD Monday – Saturday | 9:00 AM – 6:00 PM

Comprehensive Specialty Overview

High-precision diagnostics, cutting-edge medical technologies, and evidence-based treatment pathways tailored for individual patient outcomes.

SPECIALTY SCOPE • CLINICAL RATIONALE

Interstitial Lung Disease (ILD) comprises a diverse group of over 200 distinct pulmonary disorders characterized by progressive inflammation and irreversible scarring (fibrosis) of the interstitium—the microscopic tissue scaffolding that supports the delicate air sacs (alveoli). As the interstitial tissue thickens and stiffens, the lungs lose their elastic compliance and ability to transfer oxygen into the bloodstream.

Hospital Infrastructure & Safety

Accurate differentiation between idiopathic pulmonary fibrosis (IPF), environmental hypersensitivity pneumonitis, and autoimmune connective tissue-related ILD is critical for clinical preservation of lung capacity. The ILD program integrates volumetric high-resolution CT imaging, transbronchial cryobiopsy histopathology, antifibrotic pharmacotherapy, and timely lung transplant referral.

  • Dedicated Pulmonology Intervention Suite
  • Monitored Conscious Sedation & TIVA Protocols
  • 24/7 Rapid Response Thoracic ICU & ECMO

Signs & Symptoms Indicating Potential ILD

Recognizing clinical signs and diagnostic triggers that indicate the need for specialized pulmonary review.

01

Persistent Dry, Hacking, Non-Productive Cough

A chronic dry cough lasting for more than 2-3 months that fails to respond to common cough syrups, antibiotics, or allergy antihistamines.

02

Gradual, Progressive Exertional Breathlessness

Shortness of breath that creeps up over months—initially noticed only when climbing stairs or brisk walking, but gradually progressing to simple household chores.

03

"Velcro" Crackles on Chest Auscultation

Characteristic dry, fine, end-inspiratory sounds resembling the peeling apart of Velcro heard through the stethoscope over the lower lung bases.

04

Digital Clubbing (Enlargement of Fingertips)

Painless enlargement and bulbous rounding of the fingertips and toes with increased curvature of the nail beds caused by chronic tissue hypoxia.

05

Rapid Walking Oxygen Desaturation

Dropping oxygen saturation from a normal resting 96-98% down to 85-88% within 2 to 3 minutes of brisk walking on a flat surface.

06

Associated Joint Pain, Raynaud’s & Skin Changes

Cold fingers turning blue or white in cold water (Raynaud’s phenomenon), joint swelling, or skin tightening indicating underlying connective tissue disease (CTD-ILD).

Diagnostic Modalities & Treatment Protocols

Advanced medical and surgical equipment providing high-yield diagnostic precision and life-saving therapeutic interventions.

Imaging Benchmark

High-Resolution Computed Tomography (HRCT) of Chest

Volumetric thin-slice (1 mm) inspiratory and expiratory chest imaging without contrast. Identifies diagnostic radiological hallmarks: reticulation, traction bronchiectasis, ground-glass opacities, and classic subpleural basal honeycombing.

  • Differentiates Usual Interstitial Pneumonia (UIP) from NSIP patterns
  • Expiratory scans identify air-trapping in Hypersensitivity Pneumonitis
  • Prone scanning rules out dependent atelectasis
Advanced Minimally Invasive

Transbronchial Lung Cryobiopsy (TBLC)

When HRCT patterns are ambiguous, flexible bronchoscopic cryobiopsy extracts substantial, non-crushed alveolar tissue specimens under sedation, providing histological certainty without the trauma and morbidity of surgical thoracotomy.

  • Diagnostic concordance exceeding 85-90% with surgical lung biopsy
  • Avoids surgical chest drains and general anesthesia thoracotomy
  • Overnight observation with fast discharge
Disease-Modifying Therapy

Targeted Antifibrotic Pharmacotherapy

Prescription and careful monitoring of approved antifibrotic oral agents (Nintedanib / Pirfenidone) for Idiopathic Pulmonary Fibrosis and progressive fibrosing ILDs. Directly inhibits fibroblast proliferation and slows the decline in Forced Vital Capacity (FVC) by over 50%.

  • Serial liver function monitoring and dose titration
  • Proactive gastrointestinal side-effect management
  • Preserves vital lung volume and slows disease progression
Etiology Identification

Autoimmune Serological Profiling & Immunosuppression

Comprehensive screening for autoimmune rheumatic markers (ANA by IFA, extended ENA 17-antigen immunoblot, myositis profile, rheumatoid factor, anti-CCP), treating autoimmune ILD with targeted immunosuppressants (Mycophenolate Mofetil, Rituximab).

  • Avoids inappropriate high-dose steroid monotherapy in IPF
  • Joint management with rheumatology specialists
  • Preserves residual gas diffusion capacity
Functional Oximetry

Serial 6-Minute Walk Test (6MWT) & Oxygen Titration

Standardized clinical walk protocol with continuous pulse oximetry tracking exertional desaturation, distance walked, and recovery time, tailoring pulse-dose portable oxygen therapy for active daily ambulation.

  • Objective parameter tracking disease trajectory
  • Determines exact oxygen flow rate needed during exercise
  • Direct marker for lung transplant referral timing
Life-Saving Referral

Integrated Lung Transplant Pathway

Because idiopathic pulmonary fibrosis can progress unpredictably, the clinical teamintegrates early candidate workup and listing for bilateral lung transplantation, providing seamless bridging support at KIMS Hospitals.

  • Early candidacy screening before severe debility occurs
  • Pre-habilitation conditioning to maintain surgical fitness
  • Smooth transition to transplant waitlist

Structured 4-Step Clinical Protocol

How we guide every patient from initial assessment to definitive treatment and long-term functional recovery.

01

Detailed Clinical & Environmental Interview

Thorough exploration of symptom duration, bird and pigeon exposure (balcony nets, droppings), indoor dampness, mold, medications, and joint symptoms.

02

Precision HRCT & Pulmonary Function Testing

Thin-slice HRCT scan, full spirometry with DLCO (diffusion capacity for carbon monoxide), and 6-minute walk test to determine physiological impairment.

03

Multidisciplinary Discussion (MDD)

Collaborative consensus review between pulmonologist, dedicated thoracic radiologist, and pathologist to arrive at a definitive diagnosis.

04

Initiation of Antifibrotic / Immunosuppressive Therapy

Commencement of disease-modifying therapy, patient education on dietary tolerance, ambulatory oxygen setup, and pulmonary rehab enrollment.

Frequently Asked Questions

Clear, clinically accurate answers to common patient questions regarding this pulmonary specialty.

Established fibrotic scar tissue cannot be erased or reversed back into normal spongy lung tissue. However, modern antifibrotic medications (Nintedanib and Pirfenidone) significantly slow down further scar formation, halving the rate of lung capacity decline and preserving your remaining functional lung volume.

Bird Fancier’s Lung is a form of Hypersensitivity Pneumonitis triggered by inhaling aerosolized microscopic proteins from bird droppings and feathers—most commonly from pigeons nesting on apartment air-conditioner ledges and balconies in urban Bangalore. It is extremely common, often misdiagnosed as routine asthma, and requires strict pigeon avoidance and early anti-inflammatory treatment.

Because over 200 conditions cause lung fibrosis and their treatments differ dramatically (IPF requires antifibrotics and is harmed by high-dose steroids, whereas autoimmune ILD requires immunosuppressants), international guidelines mandate an MDD where the pulmonologist, specialized chest radiologist, and lung pathologist review the case together to reach the correct diagnosis.

For Idiopathic Pulmonary Fibrosis (IPF), guidelines recommend referral for lung transplant evaluation at the time of initial diagnosis, regardless of current symptoms, because disease progression can be unpredictable. For other ILDs, referral is indicated when lung capacity declines by > 10% over 6 months or when supplemental oxygen is first required.

Antifibrotics are oral capsules taken daily with meals. The most common side effects are gastrointestinal (nausea, mild diarrhea, loss of appetite) or sun sensitivity. Under proactive dietary protocols and dose titration, the vast majority of patients tolerate treatment well and continue their normal daily routines.

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